Pancreatic and Intestinal Disease in German Shepherd Dogs – What’s New?


Roger M Batt BVSc, MSc, PhD, MRCVS, DipECVIM-CA
Head of Veterinary Research
Waltham Centre for Pet Nutrition

INTRODUCTION
Pancreatic and intestinal disorders occur commonly in dogs. Signs usually include diarrhoea with or without vomiting, but changes in appetite, increased bowel sounds, excessive intestinal gas and abdominal discomfort may also be seen. Chronic pancreatic and intestinal disease may result in the so-called malabsorption syndrome, which is mainly characterised by weight loss and diarrhoea. Weight loss is occasionally the main or only sign noticed by the owner.
German shepherds dog appear to have an increased risk of chronic pancreatic and intestinal disease compared with other dog breeds. The exact cause of this is unknown but there is growing evidence that some dogs may have an immune deficiency, which predisposes them to developing intestinal disorders as well as chronic infections. In this article an overview is given of the pancreatic and intestinal diseases that are commonly seen in German shepherd dogs, and their possible causes and treatment.

COMMON INTESTINAL DISEASES
Acute versus chronic diarrhoea
Acute diarrhoea is quite common in the dog, but the actual cause is often not defined. In most cases it is probably due to dietary causes such as overeating or a sudden change of diet. The possibility of parasites should not be overlooked, especially in young dogs. Intestinal viral infections usually cause transient vomiting and diarrhoea; parvovirus used to cause more severe signs but is no longer a common problem. Bacterial infections such as Salmonella or Campylobacter occasionally cause severe, acute diarrhoea, which is more likely to occur in young and/or stressed animals. Most dogs with mild, acute diarrhoea respond well to dietary restriction alone and need no further measures taken, although young dogs should have their stool examined for parasites and be treated if necessary.
Chronic diarrhoea can be much more of a problem. It is unlikely to resolve on its own and usually requires further testing in order to determine the underlying cause (Tables 1 and 2). However, during recent years major advances have been made in the understanding of canine gastrointestinal diseases, and new and more sensitive tests have become available. These advances have particular importance for the German shepherd dog, in which several of these diseases are prevalent.

Exocrine pancreatic insufficiency (EPI)
What causes EPI?
EPI in dogs is most frequently due to pancreatic acinar atrophy, which is a condition uniquely common in the dog. It is characterised by a progressive loss of the pancreatic cells that normally produce powerful enzymes required for the initial degradation of food in the small intestine. In EPI, fewer and fewer of these digestive enzymes are produced, which ultimately leads to maldigestion and malabsorption of nutrients. The situation is compounded by the fact that there may be secondary gut damage, whereas EPI also predisposes the animal to the development of small intestinal bacterial overgrowth (SIBO), which has an additional negative effect on intestinal function.
The underlying cause of pancreatic acinar atrophy is unknown. There is a high prevalence of EPI in German shepherd dogs, in which breed the disease is reported to be heritable in an autosomal recessive manner. A recent study has indicated that the pancreatic atrophy is preceded by lymphocytic-plasmacytic inflammation, which suggests that the disease may have an immune component. However, these are very preliminary findings, and at present we have to assume that there is no definite cause, and treatment remains symptomatic.
Signs
EPI may occur in a wide variety of dog breeds and at any age, but two-third of EPI-cases in the UK are German shepherd dogs. It typically presents in young adult dogs between 1 and 5 years of age. Signs are ravenous appetite, weight loss despite the increased appetite, and diarrhoea. Stools are voluminous, poorly formed and greasy-looking. The hair coat is often in poor condition.
How to diagnose EPI
Since treatment of EPI requires lifelong replacement therapy and judicious dietary management, an exact diagnosis is important. Fortunately, this has been greatly facilitated by the availability of the TLI-test. This is a simple, reliable and sensitive blood test, which measures the amount of a pancreatic digestive enzyme (trypsinogen) in the blood stream, providing an excellent indirect assessment of pancreatic function. Dogs with EPI can be identified by a low blood TLI concentration. Marked reductions in serum TLI concentration may precede the onset of clinical signs of EPI, and assay of serum TLI has thus been useful for the early identification of affected dogs. The TLI-test has replaced stool digestion tests, which are insensitive and unreliable.
Treatment of EPI
Most dogs with EPI can be managed successfully by supplementing each meal with pancreatic enzymes. Pancreatic powdered extract seems to work best in the dog. In addition, a highly digestible, moderately fat-restricted diet should be fed, which helps to overcome residual digestive deficits. Vitamin B12 supplementation should be given to dogs with low blood concentrations of this vitamin.  Additional treatment, for instance antibiotic treatment for bacterial overgrowth, may be required in dogs that do not respond to standard management.
With adequate treatment, the outlook for dogs with EPI is usually good, although the cost of enzyme replacement can be substantial since dogs will require life-long treatment.

Small intestinal bacterial overgrowth (SIBO)
What causes SIBO?
The small intestine normally contains relatively few bacteria. Under certain circumstances there can be an increase in intestinal bacteria, which then may interfere with normal intestinal function. Bacteria can damage the intestinal mucosa (i.e. the lining of the gut), resulting in diarrhoea and weight loss, and they can also metabolise food components within the intestine, thus aggravating the weight loss.
SIBO may develop if the gut’s normal defence mechanisms are impaired. In people, it usually happens because there is decreased flow of intestinal contents due to partial obstruction, but this seems rarely to be the case in the dog. In dogs, SIBO was first described in 1983 as the cause of an enteropathy in German shepherd dogs. Since then, it has emerged as a common and important cause of chronic diarrhoea and/or weight loss in many dog breeds, although it is still decidedly more common in German shepherd dogs.
Dogs may develop SIBO secondary to EPI or gastrointestinal motility problems such as partial obstruction. It may also be a secondary complication of existing intestinal disease such as inflammatory bowel disease, where it is due to altered local immunity. Potentially, it may also occur when gastric acid production is reduced (for instance following prolonged treatment with acid-blockers), which makes the conditions in the upper small intestine less acid and more favourable for bacterial growth (Fig. 1).  However, in many cases no underlying cause can be identified. A primary or idiopathic form of SIBO is prevalent in young dogs; there is a predominance of German shepherd dogs, in which there is now good evidence that it is related to a mucosal immune deficiency. Many German shepherd dogs with bacterial overgrowth have low blood levels of IgA, which is an important immunoglobulin for mucosal defence. Intestinal IgA has been likened to an anti-absorptive paint; its primary function is to prevent antigens from bacteria, viruses and food from crossing the gut barrier. IgA-deficiency may thus predispose German shepherd dogs to SIBO and also to other, systemic infections. However, studies have been hampered by the fact that IgA in blood does not always correlate with intestinal levels. A test for faecal IgA has now been developed, which more accurately reflects intestinal IgA content. This test is still only available for research purposes, but may become more readily available in the future to identify IgA-deficient dogs that may be at increased risk for developing SIBO. Using this technique, it has already been shown that IgA-deficient German shepherd dogs have an increased incidence of persistent intestinal infections with enteropathogenic E. coli (EPEC), which may play a role in the development of SIBO.
Signs
Primary SIBO occurs typically in young adult dogs. The main clinical signs are chronic intermittent diarrhoea and weight loss or failure to gain weight. Often, signs have been present since puppy hood. Occasionally, weight loss is the only sign. Appetite may be variable but is often decreased. Affected dogs frequently have a rough, dull hair coat.
How to diagnose SIBO
A firm diagnosis of SIBO can be very difficult to make, due to the lack of sensitive and specific tests. Initial tests should eliminate other causes of diarrhoea and/or weight loss, such as intestinal parasites and pathogens, systemic disease, intestinal obstruction and EPI. Few indirect tests are then available to detect SIBO; measurement of blood folate and cobalamin concentrations may help to diagnose clear-cut cases and is easy to do in practice, but the test is not very sensitive and normal results do not rule out SIBO. Definitive diagnosis of SIBO is based on results of microbiologic culture of duodenal juice obtained during endoscopy or surgery, demonstrating increased bacterial numbers. Obviously, this is invasive, time-consuming and expensive, whereas duodenal juice culture is a specialised technique that is only available in referral institutions. However, establishing a firm diagnosis of SIBO is important especially in dogs with severe and/or recurrent signs, since they may require long-term treatment. In addition, intestinal biopsies can be taken at the time of duodenal juice collection, so that other intestinal diseases can be ruled out.
Because of the difficulties in diagnosing SIBO, much research is being done to evaluate other tests. The hydrogen breath test is relatively simple and may be helpful, but it has its limitations and is at present available in only a few places. Further tests, such as a blood test for unconjugated bile acids, are still in the early stages of development.
Treatment of SIBO
Treatment of SIBO is much more likely to be successful if an underlying cause can be identified and corrected. However, if a cause cannot be identified, treatment with antibiotics such as oxytetracycline is required, often for considerable periods of time. Many dogs respond to short-term (4 weeks) antibiotic treatment but relapse when treatment is stopped; they may then need to be treated for several months. During long-term treatment, it may be possible to reduce antibiotic dosages without causing a recurrence of clinical signs. The goal of antibiotic therapy is therefore not to sterilise the gut but to modify the intestinal flora and to encourage the establishment of less harmful bacteria. Some dogs with chronic SIBO can be difficult to manage because of recurrent diarrhoea despite appropriate antibiotic treatment. This seems to be particularly the case in German shepherd dogs, possibly because of an underlying Immune-deficiency. Failure to respond to antibiotics may furthermore be attributable to irreversible damage to the intestinal mucosa caused by the bacteria, antibiotic resistance and/or concurrent disease (for instance, inflammatory bowel disease).
Dietary management with a highly digestible, low-fat diet is important in all dogs with SIBO in order to facilitate adequate absorption of nutrients and minimize the consequences of bacterial interaction with malabsorbed fat. Additional treatment with vitamin B12 is often also necessary since SIBO can result in a very low blood B12-level, which has a negative effect on intestinal function. The diet may also be manipulated to try to change the intestinal flora towards a more normal composition. Some commercial diets now contain fructo-oligosaccharides (FOS), which are naturally occurring plant sugars. They are not digestible by the host and remain intact in the small intestine until they reach the colon, where specific bacteria break them down. FOS-supplementation may reduce the growth of potential pathogenic bacteria in the colon because they are unable to ferment it, whereas it may induce the proliferation of non-pathogenic, ‘good’ bacteria. There are only a few studies looking at the effects of dietary FOS supplementation in the dog and cat, and they do not indicate any great clinical efficacy. FOS supplementation has been used in German shepherd dogs with SIBO in an attempt to reduce bacterial numbers in the small intestine, but results have been rather dubious..
Probiotics are another potential therapeutic tool. They are a mixture of one or more harmless bacteria, usually including Lactobacilli, which are given by mouth hoping that they will colonize the small bowel, thus displacing ‘unfavourable’ microorganisms. The use of yogurt for this purpose is not recommended in dogs since this may diarrhoea worse, whereas it is unlikely that the bacteria in yogurt are able to colonize the dog gut. Studies in people suggest that probiotics can be helpful in controlling enteric pathogens, but it is unknown whether they can do the same for bacterial overgrowth.

Inflammatory bowel disease
What causes inflammatory bowel disease?
Inflammatory bowel disease is not a single disease but a group of diseases characterised by infiltration of the intestinal mucosa with inflammatory cells. The whole bowel may be affected, or only parts of it. It can be divided into different subtypes based on the main type of inflammatory cell present. The inflammation is in many cases just a non-specific immunologic response to a variety of antigens in the bowel lumen, such as parasites and bacterial pathogens, intestinal bacteria and food antigens. In some cases, this response is excessive due to an abnormally active immune system. Animals with a very permeable (leaky) gut may be more prone to developing inflammatory bowel disease, because it makes it easier for antigens to gain access to the intestinal wall.
German shepherd dogs appear to be predisposed to developing inflammatory bowel disease as well as SIBO, and it seems likely that at least in some cases there is an association between the two. It may be that the inflammatory bowel disease reflects a dysregulated intestinal immune response to the increased numbers of bacteria within the intestine. Although the breed is predisposed to developing these two diseases, there is at present no evidence that either is inherited.
Signs and diagnosis
Affected dogs usually have signs of vomiting as well as diarrhoea and weight loss. There are no specific findings on examination of faeces and blood, and diagnosis has to be made by pathologic examination of intestinal biopsies, obtained either during endoscopy or at surgery. When possible, known causes of intestinal inflammation should be identified and eliminated, particularly parasites, bacterial pathogens and food allergy. In order to exclude the latter, it is prudent to undertake a dietary trial with a selected protein diet, containing a protein the dog has not eaten recently, for a minimum of 3 weeks prior to considering further investigation using biopsy. Dogs with food allergy generally improve on such a diet but relapse when challenged with the original, offending food.
Treatment
Dietary therapy in inflammatory bowel disease is aimed at facilitating absorption of food and at reducing antigenic challenge to the gut. The diet should be highly digestible and contain one or few selected protein sources that the dog has not been exposed to recently. Other potential causes of intestinal inflammation, such as parasites and infections, should also be identified and treated if possible, and in some cases this may be enough to prevent the need for further therapy. Dogs with severe inflammatory bowel disease, however, will require additional treatment with immune-suppressive drugs, such as corticosteroids. Treatment may last weeks to months.
The role of diet in managing canine inflammatory bowel disease is likely to become more important in the future. There is increasing evidence that dietary factors, for example anti-oxidants, can be important to reduce the heightened intestinal immune response and decrease inflammation.

FUTURE CONSIDERATIONS
Where do we go from here? There is much to be learned about intestinal disease in the dog and particularly why German shepherd dogs are so predisposed to developing the above diseases. Probably the ‘hottest’ area is that of small intestinal bacterial overgrowth, with emphasis being placed on improving methods of detection and treatment. Will blood tests and/or breath tests be able to replace duodenal juice culture in the diagnosis of SIBO, and will we find a treatment alternative to prolonged antibiotic therapy? Will we be able to identify and correct IgA-deficiency before it results in clinical signs? Will we be able to diagnose and treat EPI before it is irreversible and needs indefinite enzyme supplementation? And finally, can further dietary modification give diet a greater role in the treatment of intestinal disease? There are still many questions, but the current rate of progress in biomedical science should considerably speed our progress to the answers.
 Causes of chronic diarrhoea in the dog
? Dietary sensitivity
? Parasites (worms, Giardia)
? Intestinal infections (mostly bacterial)
? Exocrine pancreatic insufficiency (EPI)*
? Small intestinal bacterial overgrowth*
? Inflammatory bowel disease*
? Other intestinal diseases (e.g. lymphangiectasia, tumours, obstructions)
? Systemic disease (e.g. liver, kidney, hormonal)

* Intestinal disorders to which German shepherd dogs are predisposed
 

 Tests for chronic diarrhoea in the dog
Baseline investigation
1. Stool examination (parasites, culture)
2. Routine blood tests (haematology, biochemistries)
3. (Optional: X-rays, ultrasound)

Investigation of EPI
4. Blood test for TLI determination

Assessment of small intestinal disease
5. Blood tests for serum folate and cobalamin
6. Response to dietary trial with selected protein diet
7. Intestinal biopsy (via endoscopy or surgical)